PReS-FINAL-2080: Overlap syndrome between primary sclerosing cholangitis and autoimmune hepatitis associated with ulcerative colitis - a case of unusual presentation in a patient with systemic juvenile idiopathic arthritis
نویسندگان
چکیده
Introduction Systemic juvenile idiopathic arthritis (systemic-JIA) is characterized by the presence of arthritis associated with systemic manifestations and an important inflammatory response, being always a clinical diagnosis of exclusion. The association of systemic-JIA with autoimmune diseases is uncommon. The authors found only one description of systemic-JIA associated with autoimmune hepatitis in a child treated with etanercept.
منابع مشابه
Evaluating distinctive features for early diagnosis of primary sclerosing cholangitis overlap syndrome in adults with autoimmune hepatitis
AIMS Overlap syndromes constitute a significant proportion of autoimmune liver disease. Our aim was to describe our cohort and evaluate practical methods of correctly diagnosing autoimmune hepatitis/primary sclerosing cholangitis overlap syndrome as early as possible clinically. METHODS 118 autoimmune hepatitis patients were screened for cholestatic liver function tests. 24 patients with chol...
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Autoimmune hepatitis (AIH), primary sclerosing cholangitis (PSC), and primary biliary cirrhosis (PBC) are chronic autoimmune liver diseases. Overlap syndrome is defined as a condition in which the clinical, biochemical, and histological features of these autoimmune diseases are overlapped. Thus, it is difficult to appreciate overlap syndrome as an actual diagnostic entity. Only a few cases of t...
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Acute-on-chronic liver failure (ACLF) is a disease in which a rapid deterioration of liver function occurs in patients with chronic liver disease, and is usually associated with a precipitating event. We present the case of a boy with autoimmune hepatitis/primary sclerosing cholangitis/ulcerative colitis (AIH/PSC/UC) overlap syndrome, in whom liver function was stable for 4.5 years of treatment...
متن کاملConcurrent autoimmune diseases in patients with autoimmune hepatitis.
BACKGROUND Although the pathomechanisms of autoimmune diseases in various organs remain unresolved, an accumulation of autoimmune diseases in individual patients has been observed. An overlap of autoimmune hepatitis (AIH) and primary biliary cirrhosis (PBC) or primary sclerosing cirrhosis has been well documented. However, the overlap of autoimmune diseases other than PBC or PSC has not yet bee...
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عنوان ژورنال:
دوره 11 شماره
صفحات -
تاریخ انتشار 2013